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Defects in Titin, the largest Human Gene, cause Chronic Congestive...
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Defects in Titin, the largest Human Gene, cause Chronic Congestive Heart Failure Henk Granzier 4, Siegfried Labeit 7, Michael Frenneaux 8, Ludwig Thierfelder 1,2
Events Archivewww.med.upenn.edu › pmi › events › events-archive
www.med.upenn.edu
Titin and MuRFs in muscle remodelling Siegfried Labeit, MD, - Professor for Experimental Medicine. Medical School, University of Heidelberg, Heidelberg ...
Möglichen neuen Ansatz für Behandlung von Herzmuskelerkrankungen...
www.mdc-berlin.de
Defekt im Muskelprotein Titin unterbricht Signalkette für Muskelkontraktion
Defekte im größten Gen des Menschen, dem Titin ...Max Delbrück Center for Molecular Medicine
www.mdc-berlin.de
— Siegfried Labeit, Universität Mannheim, entschlüsselt. Das Titin-Gen mit einer Größe, die ungefähr dem Hundertfachen eines ...
Functional genomics of chicken, mouse, and human titin supports ...journals.physiology.org › doi › ajpregu
journals.physiology.org
Siegfried Labeit. Henk Granzier. Search for more papers by this author ... Siegfried Labeit. Search for more papers by this author. Published Online:01 Aug
Titin expression in human articular cartilage and cultured...
www.em-consulte.com
... Johannes Stoeve, Hanns-Peter Scharf, Siegfried Labeit, Stefan Milz. a Laboratory for Biomechanics and Experimental Orthopedics, Department of Orthopedic ...
C-terminal titin deletions cause a novel early-onset myopathy with ...kclpure.kcl.ac.uk › portal › publications › c-termina...
kclpure.kcl.ac.uk
... Siegfried Labeit, Pascale Guicheney, France Leturcq, Mathias Gautel, Michel Fardeau, Kevin P Campbell, Isabelle Richard, Brigitte Estournet, Ana Ferreiro.
Siegfried Labeit | XanEdu Customization Platform
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Author: Siegfried Labeit. Results. Identification of a novel frameshift mutation in the giant muscle filament titin in a large Australian family with dilated ...
Elastic Filaments of the Cell - Google Books
books.google.de
Elastic filaments refer mainly to titin, the largest of all known proteins. Titin was discovered initially in muscle cells, where it interconnects the thick...
Mechanics of Elastic Biomolecules - Google Books
books.google.ca
for. elasticity. control. by. titin. in. cardiac. physiology. and. pathophysiology. HENK GRANZIER", DIETMAR LABEIT*, YIMING WU' and SIEGFRIED LABEIT" ...
Elastic Filaments of the Cellbooks.google.ae › books
books.google.ae
... Titin isoform diversity Alexandra Freiburg, Christian Witt, Jacque S Beckmann, Henk Granzier, Károly Trombitás, Carol C Gregorio, and Siegfried Labeit.
4 Material und MethodenFreie Universität Berlin
refubium.fu-berlin.de
von M Radke · · Zitiert von: 3 — Siegfried Labeit 1: :200 WB / IF. Titin anti-M8-M9. Kaninchen. Siegfried Labeit 1: :200 WB / IF. Anti-FHL2.
Titin Extensibility In Situ: Entropic Elasticity of Permanently ...Rockefeller University Press
rupress.org
von K Trombitás · · Zitiert von: 268 — Siegfried Labeit,. Siegfried Labeit. *Department of Veterinary and Comparative Anatomy, Pharmacology, and Physiology, Washington State University, Pullman, ...
Titin: An endosarcomeric protein that modulates ...Journal of Cardiac Failure
www.onlinejcf.com
von Y Wu · · Zitiert von: 40 — Siegfried LaBeit, MD†. Siegfried LaBeit. Affiliations. From the *Department of Veterinary and Comparative Anatomy, Pharmacology, and Physiology, ...
DFG GEPRIS - Mutationen im Titin als Ursache familiärer ...
gepris.dfg.de
Antragsteller: Professor Dr. Siegfried Labeit Medizinische Fakultät Mannheim der Universität Heidelberg Universitätsklinikum ...
KOPS.CARP interacts with titin at a unique helical N2A sequence and...
kops.uni-konstanz.de
ZHOU, Tiankun, Jennifer R. FLEMING, Barbara FRANKE, Julius BOGOMOLOVAS, Igor BARSUKOV, Daniel J. RIGDEN, Siegfried LABEIT, Olga MAYANS,
DFG - GEPRIS - Mutationen im Titin als Ursache familiärer ...gepris.dfg.de › gepris › projekt › ergebnisse
gepris.dfg.de
Mutationen im Titin als Ursache familiärer Muskelerkrankungen. Antragsteller Professor Dr. Siegfried Labeit Medizinische Fakultät Mannheim der Universität ...
Changes in Titin and Collagen Underlie Diastolic Stiffness HALhal.science › hal
hal.science
... Siegfried Labeit (4) , Henk Granzier (1). Afficher plus de détails. 1 WSU - Washington State University 2 PhyMedExp - Physiologie & médecine expérimentale du ...
Titin-Actin Interaction: PEVK-Actin-Based Viscosity in a Large Animal
www.hindawi.com
... Siegfried Labeit, Henk L. Granzier, "Titin-Actin Interaction: PEVK-Actin-Based ... Bogomolovas,2 Alexander Gasch,2 Carlos G. Hidalgo,1 Siegfried Labeit,2 and ...
Adaptations in Titin's Spring Elements in Normal and ...
link.springer.com
von H Granzier · · Zitiert von: 6 — Henk Granzier; Dietmar Labeit; Yiming Wu; Christian Witt; Kaori Watanabe; Sunshine Lahmers; Michael Gotthardt; Siegfried Labeit. Henk Granzier. › chapter
Adaptations in Titin’s Spring Elements in Normal and Cardiomyopathic...
link.springer.com
Henk Granzier; Dietmar Labeit; Yiming Wu; Christian Witt; Kaori Watanabe; Sunshine Lahmers; Michael Gotthardt; Siegfried Labeit. Henk Granzier. 1. Dietmar ...
Section: The Elastic Vertebrate Muscle Protein Titin; Titin as a...
link.springer.com
Titin is a giant elastic protein that functions as a molecular spring that develops passive muscle stiffness. Here we discuss the molecular basis of titin&
Wikipedia: Titin - Wikipedia
Siegfried Labeit in isolated a partial cDNA clone of titin. In 1995, Labeit and Bernhard Kolmerer determined the cDNA sequence of human cardiac titin.
Refined Localisation of the Genes for Nebulin and Titin on Chromosome...
www.nature.com
... Nigel Laing,; Bernhard Kolmerer,; Stefania Millevoi ,; Siegfried Labeit,; […] Albert de la Chapelle &; Carina Wallgren-Pettersson; -Show fewer authors.
The giant protein titin regulates the length of the striated muscle...
www.nature.com
... Medical Faculty Mannheim, MannheimGermany. Siegfried Labeit. DZHK, Mannheim-HeidelbergGermany. Siegfried Labeit.
Siegfried Labeit: H-index & Awards - Academic Profile | Research.comresearch.com › Biology and Biochemistry
research.com
Siegfried Labeit conducts interdisciplinary study in the fields of Biophysics and Cell biology through his works. Siegfried Labeit connects Titin with Obscurin ...
Molecular Medicine of the gigantic muscle protein titin filamentintegrativebio.com.ua
integrativebio.com.ua
— Siegfried Labeit: Molecular Medicine of the gigantic muscle protein titin filament ... Titin is the largest known protein with a molecular mass of ...
Changes in Titin and Collagen Underlie Diastolic Stiffness ...
hal.archives-ouvertes.fr
von Y Wu · · Zitiert von: 228 — Yiming Wu, Olivier Cazorla, Dietmar Labeit, Siegfried Labeit, Henk Granzier. Changes in Titin and Collagen Underlie Diastolic Stiffness Diversity of Cardiac ... › ha...
Adaptations in titin's spring elements in normal and cardiomyopathic ...pubmed.ncbi.nlm.nih.gov › ...
pubmed.ncbi.nlm.nih.gov
Siegfried Labeit. Affiliation. 1 VCAPP, Washington State University, Pullman, WA , USA. PMID: ; DOI: _46. Abstract.
Cardiac titin: an adjustable multi-functional spring - PubMed
pubmed.ncbi.nlm.nih.gov
The giant elastic protein titin contains a molecular spring segment that underlies the majority of myocardial passive stiffness. The mechanical characteristics...
Adaptations in titin's spring elements in normal and cardiomyopathic...
experts.arizona.edu
Henk Granzier ; Dietmar Labeit ; Yiming Wu ; Christian Witt ; Kaori Watanabe ; Sunshine Lahmers ; Michael Gotthardt ; Siegfried Labeit. 4 Citations ...
Anti-titin and antiryanodine receptor antibodies in myasthenia gravis...
moh-it.pure.elsevier.com
Fulvio Baggi, Francesca Andreetta, Carlo Antozzi, Ornella Simoncini, Paolo Confalonieri, Siegfried Labeit, Ferdinando Cornelio, Renato Mantegazza.
Changes in Titin and Collagen Underlie Diastolic Stiffness Diversity...
hal.umontpellier.fr
Yiming Wu, Olivier Cazorla, Dietmar Labeit, Siegfried Labeit, Henk Granzier. Changes in Titin and Collagen Underlie Diastolic Stiffness Diversity of Cardiac ...
Mutations of TTN, encoding the giant muscle filament titin ...
experts.arizona.edu
von B Gerull · · Zitiert von: 640 — ... Karoly Trombitás, Sabine Sasse-Klaassen, J. G. Seidman, Christine Seidman, Henk Granzier, Siegfried Labeit, Michael Frenneaux, Ludwig Thierfelder. › ...
Targeting Myocardial Disease | MDC Berlin
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The Muscle Protein Titin Regulates the Contractile Properties of the Heart
Publications
www.bme.gr
... Dittmar Labeit, Siegfried Labeit (2016) Cardiac specific titin N2B ... Alexander Gasch, Siegfried Labeit (2017) Small-molecule inhibition of ...
The giant protein titin: a major player in myocardial mechanics,...
pubmed.ncbi.nlm.nih.gov
Authors. Henk L Granzier , Siegfried Labeit. Affiliation. 1 Department of Veterinary and Comparative Anatomy, Pharmacology and Physiology, Washington State ...
Titins: giant proteins in charge of muscle ultrastructure and...
go.gale.com
Citation metadata. Authors: Siegfried Labeit and Bernhard Kolmerer. Date: Oct. 13, From: Science(Vol. 270, Issue 5234). Publisher: American Association ...
The giant muscle protein titin is an adjustable molecular ...University of Arizona
experts.arizona.edu
The giant muscle protein titin is an adjustable molecular spring. Henk L. Granzier, Siegfried Labeit. BIO5, Institute of · Molecular and Cellular Biology ...
Structure-function relations of the giant elastic protein titin in...
experts.arizona.edu
Structure-function relations of the giant elastic protein titin in striated and smooth muscle cells. Hendrikus "Henk" Granzier, Siegfried Labeit. Research output: ...
Refined Localisation of the Genes for Nebulin and Titin on ...karger.com › ejd › article › Refined-Localisation-of-...
karger.com
Siegfried Labeit;. Siegfried Labeit. (d) European Molecular Biology Laboratory, Heidelberg, Germany. Search for other works by this author on: This Site.
The giant protein titin regulates the length of the striated muscle...
accounts.public.ce.basespace.illumina.com
Paola Tonino, Balazs Kiss, Josh Strom, Mei Methawasin, John E Smith, Justin Kolb, Siegfried Labeit, Henk Granzier. The giant protein titin regulates the length ...
The giant protein titin regulates the length of the striated muscle...
pubmed.ncbi.nlm.nih.gov
The contractile machinery of heart and skeletal muscles has as an essential component the thick filament, comprised of the molecular motor myosin. The thick...
Titin-Actin Interaction: PEVK-Actin-Based Viscosity in a Large ...
cyberleninka.org
Charles S. Chung,1 Julius Bogomolovas,2 Alexander Gasch,2 Carlos G. Hidalgo,1 Siegfried Labeit,2 and Henk L. Granzier1. 1 Molecular Cardiovascular Research ... › article
Variable titin-based stiffness adjustment in heart disease —...
experts.arizona.edu
Henk L. Granzier, Yiming Wu, Karoly Trombitas, Christian Witt, Siegfried Labeit, Stephen Bell, Martin LeWinter. Physiology. Research output: Contribution to ...
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